Myelinated retinal nerve fibers are fairly common developmental abnormalities and are benign in most cases. Occasionally, associated complications including myopia, anisometropic amblyopia, strabismus, macular aplasia, and colobomas have been reported. We present a case report of a patient in whom neovascularization in a region of myelinated nerve fibers developed. These vessels caused repeated vitreous hemorrhage. Although local laser therapy was unsuccessful, panretinal ablation caused involution of the neovascularity.